డెంటిస్ట్రీ

నైరూప్య

Gardener Syndrome: A Rare Case Report

Arora M*,Deora SS,Arora P,Saluja P

Gardner syndrome (GS) is a group of diseases manifested as familial adenomatous polyposis accompanied by characteristic jaw lesions. The documented prevalence of Gardner syndrome varies from 1: 8,300 to 1: 16,000 live births in varying literatures [1]. The syndrome associated intestinal polyps have a 100% risk of malignant transformation [2]. Early identification and surgical intervention of the disease are important to prolong the life of the patient. Facial abnormalities like familial adenomatous polyposis, osteomatous jaw, ocular lesions and several dental abnormalities, and abdominal desmoid tumors are the characteristic features of this disease [1]. We elaborate a case of Gardener syndrome emphasizing on the diagnostic aspect and the management of the syndrome.